Heerfordt-Waldenström syndrome is a rare subacute variant of sarcoidosis, characterized by enlargement of the parotid or salivary glands, facial nerve paralysis. Images in Clinical Medicine from The New England Journal of Medicine — Heerfordt’s Syndrome, or Uveoparotid Fever. Heerfordt’s syndrome is a rare manifestation of sarcoidosis characterized by the presence of facial nerve palsy, parotid gland enlargement.

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A biopsy of the facial lesion was performed, and the histopathology results revealed sarcoid granulomas on the dermis Figure 3.

Loading Stack – 0 images remaining. Find articles by Neusa Yuriko Sakai Valente. The diagnosis of HWS is syndome. Author information Copyright and License information Disclaimer. The authors declare that there is no conflict of interests regarding the publication of this paper.

Some prolonged cases have been reported. Nerve granulomas and vasculitis in sarcoid peripheral neuropathy: The facial palsy of left side was categorized as HB grade III and bilateral sensorineural hearing loss was detected by pure tone audiometry Figure 4.

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View at Google Scholar T. The likelihood of permanent paralysis increases in patients who are not treated with corticosteroids. Physical examination revealed a left facial droop involving the forehead, cheek, and chin with an inability to close the left eyelid. View at Google Heerfirdt B.

The constellation of symptoms along with blood samples and biopsy usually allows the diagnosis. Ultrasound US examination showed an enlarged right parotid gland interspersed with hypoechoic areas Figure 1. Uveitis, salivary gland swelling, and facial nerve palsy in a febrile woman.

[Heerfordt syndrome].

heefrordt Abstract Sarcoidosis is a granulomatous disease of unclear etiology, which commonly presents with cough, dyspnea, chest pain, fever, weight loss, arthralgias, and erythema nodosum. Diagnosis of the syndrome is clinical, and treatment depends on the degree of systemic impairment.

This patient had marked improvement of symptoms after 4 days of prednisone therapy. Although geotropic direction-changing positional nystagmus was observed, no canal paresis was revealed by caloric test.

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[Heerfordt syndrome].

He presented with a regular general status. Find articles by Larissa Karine Leite Portocarrero. Chest, lung, abdominal, and extremity exams were unremarkable. Find articles by Priscila Kakizaki.


The Heerfordt-Waldenström syndrome as an initial presentation of sarcoidosis

NET showed no severe damage to the facial nerve. Typical clinical findings include cough, dyspnea, chest pain, fever, weight loss, arthralgias, and erythema nodosum. Support Center Support Center. PET showed hypermetabolic activity in the bilateral hilar lymph nodes, mediastinal lymph nodes, lung, spleen, and myocardium Figure 5.

Heerfordt syndrome

Sarcoidosis and its neurological manifestations. Tuberculosis, orofacial granulomatosis, and sarcoidosis are granulomatous diseases that cause unilateral facial palsy.

Presence of multinucleated cells in the granuloma right photo, hematoxylin and eosin, X Serum ACE and sIL-2R levels were elevated; however, there was no significant elevation in serum antibody for varicella zoster virus. Current approach in diagnosis and management of anterior uveitis. A year-old woman presented sydrome left facial nerve palsy, bilateral hearing loss, and swelling of her bilateral parotid glands.